Get notified of page updates

ATM Mutation: Cancer Risk

Learn about the cancer risks associated with mutations in the ATM gene. Stay up to date by signing up for our community newsletter.
Glossary on
off

Cancer Risks Associated with Inherited ATM Mutations

People with an mutation have a higher risk for several types of cancer. They tend to occur at a younger age than in people without a mutation. Experts at the National Comprehensive Cancer Network (NCCN) create guidelines which estimate the cancer risks for people with mutations. These estimates are updated based on the latest research.  

It is important to note that the cancer risks below are estimates. Your lifetime risk and risk over the next several years will vary depending on your:

  • current age.
  • sex assigned at birth.
  • specific type and location of mutation on the gene. 
  • personal and family health history.
  • diet, exercise, lifestyle and other factors.

To understand more about your personal risk, we recommend that you speak with a genetics expert who can look at these factors and help you understand your personal risk.

 

Cancer risk table

Risk estimates are averages based on research on large groups of people with different types of mutations. Some specific mutations in may have higher or lower risks. Speak with a genetics expert to better understand your risks based on your exact gene mutation type, location and other factors.

Cancer Type

Lifetime Risk with an Mutation

Lifetime Risk for General Population

Notes

Breast cancer

21 - 24%

12.5%

People with a common mutation known as c.7271T>G variant have a higher risk for breast cancer than the average risk.

Risk for 2nd breast cancer diagnosis in women who were previously diagnosed with breast cancer

4% risk within 10 years of initial diagnosis

More research is needed to confirm this risk. This applies to women who have not had mastectomy.

Male breast cancer

May be increased

.1%

More research is needed to confirm this risk.

Colorectal cancer

5 - 10%

4%

More research is needed to confirm this link.

May be increased

.8%

More research is needed to confirm this risk. Some research has shown that people with an mutation and a type of bacterial infection known as may have an increased risk for compared with people who do not have an mutation.

Ovarian cancer

2 - 3%

1.1%

Pancreatic cancer

5 - 10%

1.7%

cancer

Increased risk

13%

More research is needed to confirm this link.

Sources: NCCN Guidelines: Genetic/Familial High-Risk Assessment: Breast, Ovarian, Pancreatic, and Prostate; v.1 2027; NCCN Guidelines: Genetic/Familiar High-Risk Assessment: Colorectal, Endometrial, Esophageal, and Gastric; v.1 2026; Hall MJ, et. al. Pathogenic Variants in the Ataxia Telangiectasia Mutated () Gene are Associated with High and Moderate Risks for Multiple Cancers. Cancer Prev Res (Phila) 1 April 2021; 14 (4): 433–440; Cancer Stat Facts: Cancer. National Cancer Institute. Bethesda, MD.

Other cancers

More research is needed to better understand the lifetime risk of other cancers in people with an mutation. Because many questions about cancer risk remain unanswered, genetics experts often use a family's history of cancer and other risk factors to help people with mutations better understand their cancer risks and make informed decisions about their care.

More Resources

Find Compassionate Support

Making treatment decisions may feel overwhelming or isolating. You don't have to face this alone. Find support from people who have been there and understand. 

 

Learn More

Get Help Locating Resources

Connect with a trained volunteer who can help you navigate the decisions you face about hereditary cancer or cancer risk. 

 

Learn More

Learn More About Hereditary Cancers

Visit our section with in-depth information on screening, prevention or treatment of different types of cancer.

 

 

Learn More

Last updated September 21, 2026